A case of pseudohermaphroditism with persistence of Mullerian duct derivates in a 77-year-old patient is reported. The patient was phenotypically male and the caryotype was 46 XY. He had a normal penile size and normal sexual function until 3 years previously. The vagina and uterus communicated with the posterior urethra. Laparatomy showed an almost normal uterus with the testicles at the end of the fallopian tubes. Problems concerning embryogenesis and management are discussed.
AllenT.D.: Disorders of sexual differentiation. Clinical Pediatric urology di Kelalis, King and Belman.904–920, 1985.
2.
BartolettiR., DamiA., MortolaA., LunghiF., RizzoM.: Lo pseudoermafroditismo maschile interno: presentazione di un caso e revisione della letteratura. Acta Urol. Ital., 6: 525–527, 1989.
3.
SheehanS.J., TobbiaI.N., IsmailM.A., KellyD.G., DuffF.A.: Persistent mullerian duct syndrome. Review and report of 3 cases. Br. J. Urol., 57: 548, 1985.
