Adamantiades–Behçet's disease (ABD) is a relapsing vasculitis of unknown aetiology
and variable clinical manifestations. The syndrome can be presented in a myriad of
ways and can involve nearly every organ. Although vascular involvement is not
included among the ABD diagnostic criteria, it is a unique clinical manifestation in
adults with a potentially devastating outcome. We report an ABD case, presenting with
a thrombotic occlusion of the inferior vena cava. The authors review the recent
literature, emphasizing the spectrum of vascular manifestations accompanying Behçet's
disease.
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