Abstract
Abstract
English
La proteinosi lipidica è una rara malattia autosomica recessiva che affligge principalmente la pelle e le mucose e che viene considerata sistemica.
È caratterizzata dal deposito di materiale ialino nelle pareti arteriolo-capillari e nelle membrane epiteliali.
Viene presentato un caso di proteinosi lipidica con calcificazioni ippocampali bilaterali.
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