Worster-Drought syndrome (WDS) (congenital bilateral perisylvian syndrome, congenital pseudobulbar paresia) is characterized by neuronal migration defect, pseudobulbar paralysis, epilepsy, neuromotor retardation and perisylvian dysplasia. Pituitary abnormalities are rare disorders. We describe one case with an interesting association of congenital bilateral perisylvian syndrome with pituitary hypoplasia and posterior pituitary ectopia.
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