Spontaneous Thrombosis of Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation) Simulating Inguinal Hernia Incarceration

Abstract

Tender lumps in the inguinal region are often explored emergently to treat suspected hernial strangulation. We discuss the case of an adult male who presented acutely with a tender inguinal swelling and raised inflammatory markers and was therefore deemed as requiring surgical exploration. However preoperative abdominal computerized tomography (CT) revealed an extensive thrombosing congenital venous malformation of portosystemic origin with extension into the symptomatic inguinal canal. A potentially lethal exsanguination from surgery was thus avoided.

Keywords

Abernethy malformation congenital extrahepatic portosystemic shunt

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References

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