Erdheim–Chester disease is a rare non-Langerhans' cell histiocytosis.
Objective:
This case report is presented to familiarize clinicians with Erdheim–Chester disease and its differential diagnosis.
Results and Conclusion:
Erdheim–Chester disease presents with unique clinical and pathologic findings. Its xanthoma-like lesions can cause significant morbidity and mortality.
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References
1.
Veysser-BelotCCacoubPCaparros-LefebvreD. Erdheim–Chester disease: Clinical and radiologic characteristics of 59 cases. Medicine1996; 75:157–169.
2.
EganAJMBoardmanLATazelaarHD. Erdheim–Chester disease: Clinical, radiologic and histopathologic findings in five patients with interstitial lung disease. Am J Surg Pathol1999; 23:17–26.
3.
MillerRLSheelerLRBauerTW. Erdheim–Chester disease: Case report and review of the literature. Am J Med1986; 80:1230–1236.
4.
OnoKOshiroMUemuraII. Erdheim-Chester disease: A case report with immunohistochemical and biochemical examination. Hum Pathol1996; 27:91–95.
5.
FinkMGLevinsonDJBrownNL. Erdheim–Chester disease: A case report with autopsy findings. Arch Pathol Lab Med1991; 115:619–623.
6.
DevouassouxGLantuejoulSChatelainP. Erdheim–Chester disease: A primary macrophage cell disorder. Am J Respir Crit Care Med1998; 157:650–653.
7.
KennWEckMAllolioB. Erdheim–Chester disease: Evidence for a disease entity different from Langerhans cell histiocytosis? Three cases with detailed radiological and immunohistochemical analysis. Hum Pathol2000; 31:734–739.
8.
ZelgerBWHSidoroffAOrchardG. Non-Langerhans cell histiocytosis: A new unifying concept. Am J Dermatopathol1996; 18:490–504.
9.
SchmidtHHJGreggREShamburekMR. Erdheim–Chester disease: Low density lipoprotein levels due to rapid catabolism. Metabolism1997; 46:1215–1219.
