Left ventricular noncompaction is a relatively newly defined disorder of the endomyocardium characterized by prominent ventricular trabeculations and deep intertrabecular recesses. It is important that clinician can recognise and differentiate this condition from other forms of cardiomyopathy as treatment and prognosis may differ significantly. We report two cases of left ventricular non-compaction in the emergency department with different forms of presentations. (Hong Kong j.emerg.med. 2015;22:108-112)
MaronB.J., TowbinJ.A., ThieneG., AntselevitchC., CorradoD., ArnettD.Contemporary definitions and classification of the cardiomyopathies: an American Heart Association Scientific Statement from the Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups; and Council Epidemiology and Prevention.Circulation2006; 113(14): 1807–16.
2.
ElliottP., AnderssonB., ArbustiniE., BilinskaZ., CecchiF., CharronP.Classification of the cardiomyopathies: a position statement from the European Society of Cardiology Working Group on Myocardial and Pericardial Diseases.Eur Heart J2008; 29(2): 270–6.
3.
WaldR., BensonL.Reply to: outcome of left ventricular hypertrabeculation/noncompaction in children.Am J Cardiol2005; 96(4): 607.
4.
RitterM., OechslinE., SütschG., AttenhoferC., SchneiderJ., JenniR.Isolated noncompaction of the myocardium in adults.Mayo Clin Proc1997; 72(1): 26–31.
5.
OechslinE.N., Attenhofer JostC.H., RojasJ.R., KaufmannP.A., JenniR.Long-term follow-up of 34 adults with isolated left ventricular noncompaction: A distinct cardiomyopathy with poor prognosis.J Am Coll Cardiol2000; 36(2): 493–500.
6.
IchidaF., HammamichiY., MiyawakiT., OnoY., KamiyaT., AkagiT.Clinical features of isolated noncompaction of the ventricular myocardium.J Am Coll Cardiol1999; 34(1): 233–40.
7.
ChinT.K., PerloffJ.K., WilliamsR.G., JueK., MorhmannR.Isolated noncompaction of left ventricular myocardium: a study of eight cases.Circulation1990; 82(2): 507–13.
8.
RitterM., OechslinE., SutschG., AttenhoferC., SchneiderJ., JenniR.Isolated noncompaction of the myocardium in adults.Mayo Clin Proc1997; 72(1): 26–31.
9.
AgmonY., ConnollyH.M., OlsonL.J., KhandheriaB.K., SewardJ.B.Noncompaction of the ventricular myocardium.J Am Soc Echocardiogr1999; 12(10): 859–63.
10.
JenniR., OechslinE.N., SchneiderJ., Attenhofer JostC., KaufmannP.A.Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy.Heart2001; 86(6): 666–71.
11.
StollbergerC., FinstererJ.Pitfalls in the diagnosis of left ventricular hypertrabeculation/non-compaction.Postgrad Med J2006; 82(972): 679–83.
12.
AlhabshanF., SmallhornJ.F., GoldingF., MuseweN., FreedomR.M., YooS.J.Extent of myocardial non-compaction: comparison between MRI and echocardiographic evaluation.Pediatr Radiol2005; 35(11): 1147–51.
13.
MurphyR.T., ThamanR., BlanesJ.G., WardD., SevdalisE., PapraE.Natural history and familial characteristics of isolated left ventricular non-compaction.Eur Heart J2005; 26(2): 187–92.