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1-7 of 7 results for -keto acid dehydrogenase complex

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Research article

First published 2012-5

Clofibrate-Induced Reduction of Plasma Branched-Chain Amino Acid Concentrations Impairs Glucose Tolerance in Rats

Yoshihiro Kadota, Shunsuke Kazama, Gustavo Bajotto [...]

Journal of Parenteral and Enteral Nutrition

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Research article

First published 2010-04

DNA Carrier Testing and Newborn Screening for Maple Syrup Urine Disease in Old Order Mennonite Communities

Stephanie M. Carleton, Dawn S. Peck, Julie Grasela [...]

Genetic Testing and Molecular Biomarkers

Free access

Research article

First published 2001-3

Distribution of Key Enzymes of Branched-chain Amino Acid Metabolism in Glial and Neuronal Cells in Culture

M. Gabriele Bixel, Yoshiharu Shimomura, Susan M. Hutson [...]

Journal of Histochemistry & Cytochemistry

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Research article

First published 2018-3

CRRT: trattamento della crisi metabolica grave nella maple syrup urine disease

Pasquale Fatuzzo, Rossella R Marchese, Roberta Aliotta [...]

Giornale di Tecniche Nefrologiche e Dialitiche

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Research article

First published 2024-09

Lipid Nanoparticle mRNA Therapy Improves Survival and Reduces Serum Branched-Chain Amino Acids in Mouse Models of Maple Syrup Urine Disease

Jenny A. Greig, Matthew Jennis, Aditya Dandekar [...]

Human Gene Therapy

Free access

Research article

First published 2005-11

Status Spongiosus of White Matter in Newborn Gelbvieh-Cross Calves

D. O'Toole, D. L. Montgomery, L. Steadman [...]

Journal of Veterinary Diagnostic Investigation

Open access

Research article

First published 2025-7

Nodular Regenerative Hyperplasia Is a Frequent Finding in Explanted Livers of Patients With Maple Syrup Urine Disease

Yuan Shui, Yipeng Geng, Bita V. Naini [...]

Pediatric and Developmental Pathology