Congenital intraoral tumors derived from embryological germ layers are very rare. These lesions include teratomas, dermoids, epignathi, and teratoid tumors. These embryological neoplasms may interfere with normal development and elevation of the palatal shelves, resulting in a cleft palate. We report the case of a patient with an intraoral teratoma associated with a hemipalate deformity and describe the treatment that was carried out. The classification and sometimes the confusing terminology associated with these lesions are discussed, as are the principles of managing them.
El-MusaK.ShehadiR.ShehadiS.Surgical repair of unidirectional palatopharyngeal epignathus: case report and review of literature.Cleft Palate Craniofac J.2006; 43: 367–369.
8.
HaghighiK.MillesM.ClevelandD.ZiccardiV.Epignathus teratoma with bifid tongue and median glossal salivary mass: report of a case.J Oral Maxillofac Surg.2004; 62: 379–383.
9.
HaltermanS.M.IguladaK.N.StelnickiE.J.Epignathus: large obstructive teratoma arising from the palate.Cleft Palate Craniofac J.2006; 43: 244–246.
10.
HoltG.HoltJ.WeaverR.Dermoids and teratomas of the head and neck.Ear Nose Throat J.1979; 58: 520–531.
11.
KaplanC.PerlmutterS.MolinoffS.Epignathus with placental hydrops.Arch Pathol Lab Med.1980; 104: 374–375.
12.
LevineA.B.AlvarezM.WedgwoodJ.BerkowitzR.L.HolzmanI.Contemporary management of potentially lethal anomaly: a successful perinatal approach to epignathus.Obstet Gynecol.1990; 76: 962–966.
13.
LiangC.LaiJ.LuiC.Cleft palate with congenital midline teratoma.Ann Plast Surg.2003; 50: 515–555.
NoguchiT.JinbuY.ItohH.MatsumotoK.SakaiO.KusamaM.Epignathus combined with cleft palate, lobulated tongue, and lingual hamartoma: report of a case.Oral Surg Oral Med Oral Pathol Oral Radiol Endod.2006; 101: 481–486.
16.
VandenhauteB.LeteurtreE.Lecomte-HouckeM.PellerinP.NuytsJ.P.CuissetJ.M.Soto-AresG.Epignathus teratoma: report of three cases and a review of the literature.Cleft Palate Craniofac J.2000; 37: 83–91.
17.
YaparE.G.EkiciE.GokmenO.Sonographic diagnosis of epignathus (oral teratoma), proencephali, meromelia and oligohydramnios in a fetus trisomy 13.Clin Dysmorphol.1995; 4: 266–271.
