Acute paralysis in the context of hypokalaemia is the presenting feature of a rare group of heterogeneous disorders including the familial periodic paralyses and renal tubular acidosis. Hypokalaemic paralysis has previously been described as the presenting feature of Sjögren's Syndrome. In this report we present a patient with hypokalaemic paralysis, distal renal tubular acidosis and features suggestive of Sjögren's Syndrome.
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