Construction of a pulmonary artery pump for unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals

Abstract

Single-stage repair has been presented as the treatment of choice for pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals. This surgical approach may result in the difficult decision of whether to close the ventricular septal defect. This decision may significantly affect the postoperative course of the patient. There are several diagnostic techniques clinicians may use to help them decide if closure is indicated. One technique is to modify an extracorporeal circuit to deliver precise flow rates of blood into the newly created pulmonary arterial system, at the same time supporting the patient during the operative procedure. While this technique is not novel, there is only a single published description of the circuit. This report is brief and does not discuss potential complications that these modifications may cause. Therefore, it is the purpose of this paper to describe a circuit modification to perform this diagnostic measurement as well as elucidating potential risks of this technique.

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