Abstract
Sonographic screening of patients with Marfan syndrome (MFS) with echocardiograms and abdominal aortic sonography has become the standard of care to monitor aneurysm and/or dissection development. These anomalies are the leading cause of morbidity and mortality related to this syndrome. Other cardiovascular changes associated with MFS include mitral valve prolapse leading to severe mitral regurgitation and dilation of the aortic root at the sinus of Valsalva. Careful interval follow-up using modern sonographic equipment ensures that any significant vascular changes will be detected. This case documents a finding of an aberrant aneurysmal artery branching off the abdominal aorta discovered during annual follow-up screening of a patient with Marfan syndrome. This aneurysmal artery was subsequently found by computed tomographic angiography to be supplying an intralobar lung sequestration.