Survival of Three Neonates With Congenital Diaphragmatic Hernia and d-Transposition of the Great Arteries

Abstract

Survival is significantly compromised in infants born with congenital diaphragmatic hernia and major cardiac anomalies. Mortality is highest when congenital diaphragmatic hernia occurs in association with d-transposition of the great arteries. We present three infants with congenital diaphragmatic hernia associated with d-transposition of the great arteries from a single institution. All three infants survived to discharge after surgical repair/palliation of both the diaphragmatic hernia and heart defect and are doing well at last follow-up. The clinical course and management of these three patients are described.

Keywords

d-Transposition of the great arteries congenital diaphragmatic hernia congenital heart disease arterial switch operation

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