Moyamoya disease is a rare cerebrovascular occlusive disorder most often found among the Japanese. It is angiographically defined as a progressive steno-occlusion of the bilateral internal carotid arteries with characteristic abnormal vascular networks, so-called Moyamoya vessels, at the base of the brain. MRI is the initial investigation of choice and we describe an MRI sign to diagnose Moyamoya disease warranting digital subtraction angiography.
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