Osteogenic Sarcomatous Degeneration of the Temporal Bone Squama in Paget's Disease

Abstract

Paget's bone disease is a common disorder affecting approximately 3–4% of the population over 40 and up to 10–11% of the population older than 80 years. It is characterized by excessive and abnormal bone remodelling. The disease predominates in bones containing red marrow, with a clinical course characterized by active and quiescent periods; pelvis, sacrum, spine and skull are the most affected parts. We report the case of a 79-year-old woman with polyostotic Paget's disease who had a focal sarcomatous degeneration diagnosed by CT and MR.