Behçet's disease is an uncommon systemic process of unknown etiology that appears most often in Mediterranean and Asiatic countries. Arterial or venous involvement is rare. Arterial findings are occlusions, aneurysms, and rarely, pseudoaneurysms of the aorta, pulmonary, peripheral , and visceral arteries. The authors report a case characterized by typical cutaneous and orogenital manifes tations in a young man with severe anemia and hypotension. Arteriographic study showed a right femoral pseudoaneurysm. An end-to-end saphenous vein graft from the external iliac to superficial femoral arteries was performed. After six months of follow-up the patient remains well.
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