Novel Technique for Treatment of a Renal Artery Occlusion in a Child With Neurofibromatosis: A Combined Endovascular and Laparoscopic Approach

Abstract

Neurofibromatosis is associated with mid-aortic dysplasia, renal artery aneurysms and renal artery ostial stenosis, or occlusions in about 1% of cases. We describe a novel approach to recanalize an occluded renal artery in a 10-year-old girl with neurofibromatosis and difficulty in pharmacologically controlling her hypertension. Normally, when reconstruction is required, an open operative technique is used. We report on the combined use of laparoscopic exposure and percutaneous retrograde puncture of the occluded renal artery, which could be recanalized and stented. The pros and cons of this new approach are discussed.

Keywords

Neurofibromatosis renovascular hypertension renal angioplasty renal stent

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