Parry-Romberg Syndrome with Contralateral and Ipsilateral Extremity Involvement

Abstract

Background:

The Parry-Romberg syndrome is an acquired progressive hemifacial atrophy involving the subcutaneous tissues of the scalp and face. Involvement of the extremities is uncommon in this syndrome.

Objective:

A case of contralateral and ipsilateral extremity involvement in the Parry-Romberg syndrome is reported, and the difficulties in distinguishing this syndrome from linear scleroderma en coup de sabre are reviewed.

Methods:

A MEDLINE search for cases of Parry-Romberg syndrome with contralateral extremity involvement was performed and the cases reviewed.

Results:

Contralateral extremity involvement in the Parry-Romberg syndrome is rare.

Conclusion:

This may be the first case reported in the English literature of Parry-Romberg syndrome with contralateral and ipsilateral extremity involvement.