Seven members of the same family suffering from Groenow I granular dystrophy and associated congenital cataracts have been studied.
Three patients had corneal dystrophy at various stages and trhee others had a fetal nuclear congenital cataract. A penetrating keratoplasty button was studied under light and electron microscopies. This association has not been described previously. However we must emphasize that there is no general validity for a correlation between granular dystrophy and congenital cataract.
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2.
WaringG.O., RodriguesM.M.III, LaibsonP.R.Corneal dystrophies of the epithelium, Bowman's layer and stroma.Surv Ophthalmol1978; 23: 71–5.
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AkiyaS., BrownS.I.Granular dystrophy of the cornea (characteristic electron microscopic lesion).Arch Ophthalmol1970; 84: 179–92.
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JohnsonB.L., BrownS.I., ZaidmanG.W.A light and electron microscopic study of recurrent granular dystrophy of the cornea.Am J Ophthalmol1981; 92: 49–58.
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RodriguesM.M., StreetenB.W., KrachmerJ.H.Microfibrillar protein and phospholipid in granular corneal dystrophy.Arch Ophthalmol1983; 101: 802–4.
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SorsonE.T.Granular dystrophy of the cornea. An electron microscopic study.Am J Ophthalmol1965; 59: 1001–7.
