Natural killer (NK) cell lymphoma is a progressive non-Hodgkin’s lymphoma with rare prevalence. Intraocular involvement of NK cell lymphoma is very rare, with only case reports to date.
Case presentation:
Here, we report a case of intraocular involvement of NK cell lymphoma which was presented with bilateral uveitis, iris mass, and diffuse infiltration into the center nerve system (CNS), skin, and possibly myocardium.
Conclusions:
Iris mass and uveitis which is not responsive to steroids may be ocular manifestations of intraocular lymphoma, such as NK cell lymphoma. Ophthalmological and systemic examinations should be required for early diagnosis and treatment.
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