To describe the clinical manifestations in a patient with Sjögren reticular dystrophy of the retinal pigment epithelium, and the evolution of the disease over a 20-year follow-up period.
Case Report
A 45-year-old woman with Sjögren reticular dystrophy of the retinal pigment epithelium was seen for the first time in 1983; the patient underwent 20 years of annual check-ups.
Results
Over the follow-up period, fundus photographs, computerized perimetry, electroretinogram, and electro-oculogram findings had either normal or slightly subnormal outcome.
Conclusions
The results confirm that this disease involves only the retinal pigment epithelium and should not be considered a central tapeto-retinal degeneration or late onset retinopathy.
KinghamJ.D.FenzlR.E.WillersonD.AabergT.M.. Reticular dystrophy of the retinal pigment epithelium. A clinical and electrophysiologic study of three generations.Arch Ophthalmol1978; 96: 1177–84.
3.
BlodiF.C.. The pathology of central TRD (hereditary macular degeneration).Trans Am Acad Ophthalmol Otolaryngol1966; 70: 1047–53.
4.
WaardenburgP.J.. Genetics and Ophthalmology, vol. 2. Assen, Netherlands: Royal van Gorcum; 1963: 1685–6.
5.
HsiehR.C.FineB.S.LyonsJ.S.. Patterned dystrophies of the retinal pigment epithelium.Arch Ophthalmol1977; 95: 429–35.
6.
DeutmanA.F.RumkeA.M.L.. Reticular dystrophy of retinal pigment epithelium.Arch Ophthalmol1969; 82: 4–9.
7.
AlezzandriniA.A.. La retino-Fluoresceinografia en las alteraciones del epitelio pigmentario de la retina.Arch Ophthalmol1971; 46: 13–20.
8.
FishmanG.A.WoolfM.B.GoldbergM.F.BusseB.. Reticular tapeto-retinal dystrophy as a possible late stage of Sjögren's reticular dystrophy.Br J Ophthalmol1976; 60: 35–40.
9.
DonnelF.E.SchatzH.ReidP.GreenW.R.. Autosomal dominant dystrophy of the retinal pigment epithelium.Arch Ophthalmol1979; 97: 680–3.
10.
GirardP.SetbonG.ForestA.CoscasG.. Dystrophies en réreau de l'epithélium pigmentaire (dystrophies macroreticulaires et en aile de papillon).J Fr Ophtalmol1980; 3: 101–6.
11.
MarmorM.F.ByersB.. Pattern dystrophy of the retinal pigment epithelium.Am J Ophthalmol1977; 84: 32–44.
12.
CortinP.ArcherD.MaumeneeJ.H.FejockK.SperosP.. A patterned macular dystrophy with yellow plaques and atrophic changes.Br J Ophthalmol1980; 64: 127–34.
13.
MaranoF.DeutmanA.F.PinckersA.J.AandekerkA.L.RjjneveldW.J.. Reticular dystrophy of the retinal pigment epithelium and choroidal neovascularization. A fluorescein and ICGV study.Acta Ophthalmol1997; 75: 22–7.
