A patient with carotid-cavernous sinus fistula associated with fibromuscular dysplasia, who died from rupture of an associated splenic aneurysm despite successful treatment of the CCF, is reported. When multivessel involvement with aneurysmal dilatation is observed in patients with fibromuscular dysplasia, the possibility of aneurysm ruptures in any of the arteries should be considered.
BellotJ.GherardiR.PoirierJ.LacourP.DebrunG.BarbizetJ.: Fibromuscular dysplasia of cervicocephalic arteries with multiple dissections and a carotid-cavernous fistula. Stroke16 (1985), 255.
2.
ClaiborneT. S.: Fibromuscular hyperplasia. Report of a case with involvement of multiple arteries. Am. J. Med.49 (1970), 103.
3.
HieshimaG. B.CahanL. D.MehringerC. M.BentsonJ. R.: Spontaneous arteriovenous fistulas of cerebral vessels in association with fibromuscular dysplasia. Neurosurgery18 (1986), 454.
ManelfeC.ClariesseJ.FredyD.: Fibromuscular dysplasia of the cervico-cephalic arteries. Report of 70 cases. J. Neuroradiol.1 (1974), 149.
7.
MettingerK. L.EricsonK.: Fibromuscular dysplasia and the brain. Observations on angiographic, clinical and genetic characteristics. Stroke13 (1982), 46.
