CPB management of G6PD deficient patient – a case report

Glader BE . Glucose-6-phosphate dehydrogenase deficiency and related disorders of hexose monophosphate shunt and glutathione metabolism. In: Wintrobe’s Clinical Hematology. 10th ed. Baltimore: Williams & Wilkins; 2008: 1176–1190.

Luzzatto L Metha A Vulliany T . Glucose-6-phosphate dehydrogenase deficiency. In: Scriver CR Beaudet AL Sly WS , eds. The Metabolic and Molecular Basis of Inherited Disease. 8th ed. Columbus: McGraw-Hill; 2001: 4517–4553.

Cappellini MD Fiorelli G . Glucose-6-phosphate dehydrogenase deficiency. Lancet 2008; 371: 64–74.

Gerrah R Shargal Y Elami A . Impaired oxygenation and increased hemolysis after cardiopulmonary bypass in patients with glucose-6-phosphate dehydrogenase deficiency. Ann Thorac Surg 2003; 76: 523–527.

World Health Organization. Working group glucose-6-phosphate dehydrogenase deficiency. Bull WHO. 1989; 67: 601–611.

Elyassi AR Rowshan HH . Perioperative management of the glucose-6-phosphate dehydrogenase deficient patient: a review of literature. Anesth Prog 2009; 56: 86–91.

Swindell CG Barker TA McGuirk SP . Washing of irradiated red blood cells prevents hyperkalaemia during cardiopulmonary bypass in neonates and infants undergoing surgery for complex congenital heart disease, Eur J Cardiothorac Surg 2007; 31: 659–664.

Allen BS Rahman S Ilbawi MN . Detrimental effects of cardiopulmonary bypass in cyanotic infants: preventing the reoxygenation injury. Ann Thorac Surg 1997 Nov; 64(5): 1381–87.

Russell James A. Navickis Roberta J. Wilkes Mahlon M. Albumin versus crystalloid for pump priming in cardiac surgery: meta-analysis of controlled trials. J Cardiothorac Vasc Anesth 2004: 18(4): 429–437.

Schroeder VA Pearl JM Schwartz SM Combined steroid treatment for congenital heart surgery improves oxygen delivery and reduces postbypass inflammatory mediator expression. Circulation 2003; 107: 2823–2828.

Munoz R Laussen PC Palacio G . Changes in whole blood lactate levels during CPB for surgery for congenital cardiac disease: an early indicator of morbidity and mortality. J Thorac Cardiovasc Surg 2000; 119: 155–162.

Larsen M Webb G Kennington S . Mannitol in cardioplegia as an oxygen free radical scavenger measured by malondialdehyde. Perfusion 2002; 17; 51–55.

Rawn DJ Harris HK Riley JB Yoda DN Blackwell MM . An under-occluded roller pump is less hemolytic than a centrifugal pump. J Extra Corpor Technol 1997 Mar; 29(1): 15–18.

He D Hou L . Effects of high dose ascorbic acid on haemostasis during and after cardiopulmonary bypass, Perfusion 1988; 3; 281–286.

Dogra N Puri GD SS Rana SS . Glucose-6-phosphate dehydrogenase deficiency and cardiac surgery, Perfusion 2010; 25(6): 417–421.