Acanthosis nigricans has been classified in different ways. All classifications depend on the clinical picture and the association with other conditions.
Objective
We report a case of acanthosis nigricans in a patient with Kabuki syndrome. This syndrome is characterized by five main manifestations: typical facial features, post natal growth deficiency, skeletal abnormalities, dermatoglyphic abnormalities, and mild to moderate mental retardation.
Conclusion
Our case may suggest that acanthosis nigricans could be associated with Kabuki syndrome.
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