Abstract
Purpose
We report the case of a patient with IgG4-related disease with multiple organ involvement, especially myocardium, that was successfully treated with prednisone.
Methods
We performed several serological tests, electrocardiogram, echocardiography, computed tomography and inguinal lymph node biopsy.
Results
We diagnosed the patient with IgG4-related disease by the elevated serum IgG4 level and histological lymph node findings.
Conclusions
This is the first reported case of IgG4-related disease with dilated cardiomyopathy.
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