Abstract
Summary
The MPS present in the urines of 3 patients with Morquio-Ullrich's disease have been studied. In all 3 cases a substantial amount of KS has been identified. The identification has been based on chemical, chromatographic and infrared data. This MPS has hitherto never been identified in urine, either normal or pathological. Neither ChS B or HMS was found in the urines of these children. The metabolic disorder of the MPS in Morquio-Ullrich's disease appears to be different from that observed in Hurler's disease.
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