Longitudinal ulnar deficiency, whose detailed anatomy is varied, is often accompanied by other abnormalities and appears as part of several syndromes. The history of its classification is reviewed, and the treatments, which have been offered, described.
Follow-up of a series shows that the function achieved is good and is optimised by aids, occupational therapy and some hand surgical procedures. The more elaborate surgical reconstructions are unlikely to be beneficial.
References
1.
Birch-JensonA. Congenita] deformities of the upper extremities. Andelsbogtrykkerriet, OdenseDenmark1949; p46–47
2.
BlairW. F.ShurrD. G.BuckwalterJ. A. Functional status in ulnar deficiency. J. Pediatr. Orthop.1983; 3: 37–40
JohnsonJ.OmerG. E. Congenital ulnar deficiency. Natural history and therapeutic implications. Hand Clin.1985; 1(3)
6.
KitanoK.TadaK. One bone forearm procedure for partial defect of the ulna. J. Pediatr. Orthop.1985; 5: 290–293
7.
KummelW. Die missbildugen der extremitaeten durch defekt Verwachsung und Ueberzahl. Biblioteca Medica, Section E, Vol. 3, CassellT. G.. Fischer and Co. 1895
8.
MarcusN.OmerG. Carpal deviation in congenital ulnar deficiency. J. Bone Joint Surg.1984; 66A: 1003–1007
9.
OgdenJ. A.WatsonH. K.BohneW. Ulnar dysmelia. J. Bone Joint Surg.1976; 58A: 467–475
10.
RigaultP.TouzetP.PadovaniJ. P.MaroteauxP.FinidortG.ChaumienD. P. Les hypoplasies et aplasies du cubitus chez l'enfant. Echonelies longitudinales internes du membre superieur. Etude de 38 cas chez 31 enfants. Chirurgie1985; 111: 692–700
11.
SwansonA.TadaK.YonenobuK. Ulnar ray deficiency: its various manifestations. J. Hand Surg1984; 9 A: 658–664
