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Abstract

Objective

Congenital bony syngnathia is an extremely rare condition characterized by bony fusion of the jaws. Five new cases are described and the existent literature is reviewed. A classification system is proposed and treatment recommendations based on this classification are presented.

Keywords

classification system congenital bony syngnathia

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References

Aorawal

, Chandra

S.S.

, Sreekumar

N.S.

Congenital bilateral intermaxillary bony fusion, Ann Plast Surg 1993; 30: 163–166.

Alfery

D.D.

, Ward

C.F.

, Harwood

J.R.

, Mannino

F.L.

Airway management for a neonate with congenital fusion of the jaws.

Anesthesiology 1979; 51: 340–342.

Alvarez

G.E.

The aglossia-adactylia syndrome.

Br J Plast Surg 1976; 29: 175–178.

Brown

D.M.

, Marsh

J.L.

Agnathia and associated malformations: A case report.

Cleft Palate J 1990; 27: 415–418.

Burket

L.W.

Congenital bony temporomandibular ankylosis and facial hemiatrophy.

J Am Med Assoc 1936; 106: 1719–1722.

Dobrow

Syndrome identification case report 96. Syngnathia and multiple defects.

J Clin Dysmorphol 1983; 1(2): 5–7.

Gartlan

M.G.

, Davies

, Smith

R.J.

Congenital oral synechiae.

Ann Otol Rhinol Laryngol 1993; 102: 186–197.

Goodacre

T.E.

, Wallace

A.F.

Congenital alveolar fusion.

Br J Plast Surg 1990; 43: 203–209.

Hamamoto

, Matsumoto

A case of facio-genito-popliteal syndrome.

Ann Plast Surg 1984; 13: 224–229.

10.

Hegtvedt

A.K.

Diagnosis and management of facial asymmetry, In: Peterson

, ed. Principles of oral and maxillofacial surgery. Philadelphia: JP Lipincott, 1992; 1400–1401.

11.

Hochstetter

(1948), cited in Goodacre TE, Wallace AF. Congenital alveolar fusion.

Br J Plast Surg 1990; 43: 203–209.

12.

Hoggins

G.S.

Aglossia congenita with bony fusion of the jaws.

Br J Oral Surg 1969; 7: 63–65.

13.

Kittur

S.D.

, Weaver

D.D.

, Maves

M.D.

Syndrome identification report 95. Congenital fusion of the gums and jaws.

J Clin Dysmorphol 1983; 1(2): 2–4.

14.

Miskinyar

S.A.

Congenital mandibulo-maxillary fusion.

Plast Reconstr Surg 1979; 63: 120–121.

15.

Nanda

Maxillomandibular ankylosis and cleft palate in rat embryos.

J Dent Res 1970; 49: 1086–1090.

16.

Narasimharao

, Mitra

S.K.

Congenital fusion of the gums with ankylosis of temporomandibular joints.

Indian Pediatr 1984; 21: 656–657.

17.

Nwoku

A.L.

, Kekere-Ekun

T.A.

Congenital ankylosis of the mandible.

J Maxillofac Surg 1986; 14: 150–152.

18.

Petterson

Aglossia congenita with bony fusion of the jaws.

Acta Chir Scand 1961; 122: 93–95.

19.

Poswillo

The pathogenesis of the first and second branchial arch syndrome.

Oral Surg Oral Med Oral Pathol 1973; 35: 302–328.

20.

Robinow

, Marsh

J.L.

, Edgerton

M.T.

. Discordance in monozygotic twins for aglossia-adactylia, and possible clues to the pathogenesis of the syndrome. Birth Defects 1978; 14(6A): 223–230.

21.

Salleh

N.M.

Congenital partial fusion of the mandible and maxilla.

Oral Surg Oral Med Oral Pathol 1965; 20: 74–76.

22.

Shah

R.M.

Palatomandibular and maxillo-mandibular fusion, partial aglossia and cleft palate in a human embryo.

Teratology 1977; 15: 261–272.

23.

Simpson

J.R.

, Maves

M.D.

Congenital syngnathia or fusion of the gums and jaws.

Otolaryngol Head Neck Surg 1985; 93: 96–99.

24.

Snijman

P.C.

, Prinsloo

J.G.

Congenital fusion of the gums, Am J Dis Child 1966; 112: 593–595.

25.

Sternberg

, Sagher

, Golan

. Congenital fusion of the gums with bilateral fusion of the temporomandibular joints. Plast Reconstr Surg 1983; 72: 385–387.

26.

Tessier

Anatomical classification of facial, craniofacial and laterofacial clefts.

J Maxillofac Surg 1976; 4: 69–92.

Congenital Bony Syngnathia: A Proposed Classification

Abstract

Objective

Keywords

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