Familial chylomicronemia syndrome is a disease characterised by hypertriglyceridemia and chylomicronemia. In recent years, carnitine has been used in the treatment of hyperlipidemia and it is reported to be highly effective. We report a patient presenting with acute pancreatitis who through testing was diagnosed with familial chylomicronemia syndrome. We found the use of carnitine treatment in familial chylomicronemia syndrome to be highly effective.
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