JDMS Article - SDMS CME Credit

Article: Sirenomelia With Anhydramnios: A Clue From the Movements of Fetal Limbs

Authors: Rahul Dev Chauhan, MD, Ipsita Sahoo, MD, and Yashvir Mathur, MD

Category: OB/GYN [OB]

Credit: 0.75 SDMS CME Credit

Objectives: After studying the article entitled “Sirenomelia With Anhydramnios: A Clue From the Movements of Fetal Limbs,” you will be able to:

1. Describe the anomalies associated with sirenomelia

2. Understand the different methods used to classify sirenomelia

3. Understand the importance of evaluation of independent lower limb movements in patients with oligohydramnios or anhydramnios

1. Sirenomelia is typically characterized by the:

2. Fusion of upper limbs, single umbilical artery, and cardiac anomalies

3. Fusion of lower limbs, single umbilical artery, and anomalies of the lower spine and urogenital and lower gastrointestinal tracts

4. Fusion of lower limbs, anomalies of the lower spine and urogenital and lower gastrointestinal tracts, and cardiac anomalies.

What is the typical appearance of Potter facies?

Micrognathia, flattened nose, low-set ears

Micrognathia, cleft palate, flattened nose

Frontal bossing, micrognathia, low-set ears

Microcephaly, micrognathia, flattened nose

Which patient demographics are at higher risk of sirenomelia?

Pregnant women who consume alcohol during pregnancy

Older maternal ages (over 40 years) who take seizure medication

Pregnant women exposed to >50 rads of radiation

Younger and old maternal ages (under 20 and over 40 years)

How could sirenomelia be classified on a fetus without feet?

Phocomelia

Sympus dipus

Sympus monopus

Sympus apus

The authors were able to make the diagnosis of sirenomelia using ultrasound to demonstrate:

Severe oligohydramnios

The absence of independent movement of the lower limbs from one another

Renal agenesis

The lower legs in a “cross-legged” position