Abstract

Article: First-Trimester Diagnosis of Hypoplastic Left Heart Syndrome: A Case Report
Authors: Emily Hildebrand, BSDMS, RDMS, RDCS, RVT
Category: Cardiac (Fetal) [FE]
Credit: 1.0 SDMS CME Credit
Objectives: After studying the article entitled “First-Trimester Diagnosis of Hypoplastic
Left Heart Syndrome: A Case Report,” you will be able to:
Know that hypoplastic left heart syndrome (HLHS) is a spectrum of left-sided heart anomalies resulting from outflow or inflow obstruction
Understand HLHS is a lethal cardiac anomaly if not treated in the first week of life
Describe the sonographic features that could aid in early detection of HLHS
What is the most common cause of underdevelopment of the left ventricle? Outflow obstruction of the aortic valve Inflow obstruction of the tricuspid valve Inflow obstruction of the mitral valve Outflow obstruction of the pulmonic valve
What percentage of congenital heart disease does HLHS comprise? 1% 5% 9% 14%
What is the purpose of the patent foramen ovale and patent ductus arteriosus in a fetus? Perfuse the liver Perfuse the lungs Bypass the liver Bypass the lungs
Which fetal circulation connection needs to remain patent after birth in newborns with HLHS? Ductus arteriosus Hypogastric arteries Ductus venosus Foramen ovale
What is the name of the first stage of surgical repair for HLHS? Balloon septostomy Norwood procedure Glenn shunt Fontan operation
What is the mortality rate (%) of untreated HLHS? 25% 50% 75% 100%
Which of the following diagnoses is the most common differential and seen in conjunction with HLHS? Interrupted aortic arch Absent ductus venosus Aortic coarctation Ductus arteriosus closure
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