We report a case of Klippel-Trenaunay-Weber syndrome in a 31-year-old woman who presented with hypertrophy of the left leg. She had severe osteoarthritic changes in the left hip joint secondary to the lack of acetabular coverage of the femoral head as the result of lateral inclination of the pelvis owing to leg-length discrepancy of 4 cm. The centre-edge angle (coverage ratio of the acetabulum to the femoral head) was improved from 15° to 33° after a foot lift. She underwent osteotomy and lengthening of the normal contralateral tibia using a Taylor spatial frame. Hip arthroplasty could be avoided as osteoarthritic changes of the hip joint had improved.
LindenauerSM. The Klippel-Trenaunay syndrome: Varicosity, hypertrophy and hemangioma with no arteriovenous fistula. Ann Surg1965;162:303–14.
4.
CravenNWrightAL. Familial Klippel-Trenaunay syndrome: A case report. Clin Exp Dermatol1995;20:76–9.
5.
BaskervillePAAckroydJSBrowseNL. The etiology of the Klippel-Trenaunay syndrome. Ann Surg1985;202:624–7.
6.
BaskervillePAAckroydJSThomasLea MBrowseNL. The Klippel-Trenaunay syndrome: Clinical, radiological and haemodynamic features and management. Br J Surg1985;72:232–6.
7.
BallockRTWiesnerGLMyersMTThompsonGH. Hemihypertrophy. Concepts and controversies. J Bone Joint Surg Am1997;79:1731–8.
8.
FraumeniJFJrMillerRW. Adrenocortical neoplasms with hemihypertrophy, brain tumors, and other disorders. J Pediatr1967;70:129–38.
9.
DemetriadesDHagerJNikolaidesNMalamitsi-PuchnerABartsocasCS. Proteus syndrome: Musculoskeletal manifestations and management: A report of two cases. J Pediatr Orthop1992;12:106–13.
10.
GagliardiGGMahanKT. Melorheostosis: A literature review and case report with surgical considerations. J Foot Ankle Surg2010;49:80–5.
GloviczkiPHollierLHTelanderRLKaufmanBBiancoAJSticklerGB. Surgical implications of Klippel-Trenaunay syndrome. Ann Surg1983;197:353–62.
13.
LealJDaviesAPSelmiTANeyretP. Knee arthroplasty in Klippel-Trenaunay syndrome: A case presentation with 5 years follow-up. J Arthroplasty2008;23:623–6.
14.
MatsubaraHTsuchiyaHSakurakichiKWatanabeKTomitaK. Deformity correction and lengthening of lower legs with an external fixator. Int Orthop2006;30:550–4.
15.
WatanabeKTsuchiyaHSakurakichiKMatsubaraHTomitaK. Double-level correction with the Taylor Spatial Frame for shepherd's crook deformity in fibrous dysplasia. J Orthop Sci2007;12:390–4.
