Pulmonary atresia with intact ventricular septum (PA-IVS) and myocardial dysfunction is a challenging entity to manage. Presented is a patient with PA-IVS who developed myocardial dysfunction and heart failure following an episode of periprocedural hypotension. He was successfully treated with a single ventricle assist device (SVAD) placed without cardiopulmonary bypass and a ductal stent as a bridge to donation after circulatory death heart transplant. This report describes the technique of SVAD placement without cardiopulmonary bypass.
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References
1.
YoshimuraNYamaguchiM.
Surgical strategy for pulmonary atresia with intact ventricular septum: initial management and definitive surgery. Gen Thorac Cardiovasc Surg.2009;
57(
7):
338-
346.
2.
FreedomRMAndersonRHPerrinD.
The significance of ventriculo-coronary arterial connections in the setting of pulmonary atresia with an intact ventricular septum. Cardiol Young.2005;
15(
5):
447-
468.
3.
BleiweisMSPhilipJFudgeJC, et al.Support with single ventricle-ventricular assist device (sVAD) in patients with functionally univentricular circulation prior to Fontan operation. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu2023:
26:
26-
39.
4.
TownsendMJeewaAAdachiI, et al.Ventricular assist device use in patients with single-ventricle circulation. Can J Cardiol.2022;
38(
7):
1086-
1099.
5.
BleiweisMSFudgeJCPeekGJ, et al.Ventricular assist device support in neonates and infants with a failing functionally univentricular circulation. JTCVS Tech.
2021;
13:
194-
204.
