Circumflex aorta is described as a retroesophageal aortic arch, with opposite-sided descending aorta forming a true vascular ring with ligamentum arteriosum. We report two cases of right-sided circumflex aorta with varied clinical presentation. Computed tomography diagnosed this vascular ring anomaly. The patients were managed with the aortic uncrossing procedure as a primary surgical strategy. Preoperative diagnosis and thorough planning were essential for the successful outcome. The patients did not have any residual symptoms of tracheal and esophageal compression on follow up.
Get full access to this article
View all access options for this article.
References
1.
BravoCGámezFPérezR, et al.Fetal aortic arch anomalies. J Ultrasound Med. 2016;35(2):237-251.
2.
HaranalMSrimuruganBSivalingamS. Circumflex aorta: an uncharted territory. Asian Cardiovasc Thorac Ann. 2022;30(2):217-225.
RussellHMRastatterJCBackerCL. The aortic uncrossing procedure for circumflex aorta. Oper Tech Thorac Cardiovasc Surg. 2013;18(1):15-31.
5.
BaderVKnightWBDantonMHPengE. Congenital arch malformation: a review of morphology and surgical management of circumflex aortic arch. Vessel Plus. 2020;4:34. doi:10.20517/2574-1209.2020.36
6.
PriyaSThomasRNagpalPSharmaASteignerM. Congenital anomalies of the aortic arch. Cardiovasc Diagn Ther. 2018;8(S1):S26-S44.
7.
KamranAFriedmanKGJenningsRW, et al.Aortic uncrossing and tracheobronchopexy corrects tracheal compression and tracheobronchomalacia associated with circumflex aortic arch. J Thorac Cardiovasc Surg. 2020;160(3):796-804.
