Anatomic single coronary arteries are quite rare but can be a potential cause of sudden cardiac death. We present the first case of a pediatric patient with an anatomic single right coronary artery (Lipton type R1 or Shirani-Roberts type IIA), of a type which has been associated with adult-onset ischemic cardiac disease. We review the evaluation and management of this young patient.
VillaADSammutENairARajaniRBonaminiRChiribiriA. Coronary artery anomalies overview: the normal and the abnormal. World J Radiol. 2016;8(6):537–555.
3.
LiptonMJBarryWHObrezISilvermanJFWexlerL. Isolated single coronary artery: diagnosis, angiographic classification, and clinical significance. Radiology. 1979;130(1):39–47.
4.
ShiraniJRobertsWC. Solitary coronary ostium in the aorta in the absence of other major congenital cardiovascular anomalies. JACC. 1993;21(1):137–143.
5.
SmithJC. Review of single coronary artery with report of 2 cases. Circulation. 1950;1(5):1168–1175.
6.
SharbaughAHWhiteRS. Single coronary artery. Analysis of the anatomic variation, clinical importance, and report of five cases. JAMA. 1974;230(2):243–246.
7.
UpadhyayaSGNMughalLHConnollyDLipG. Single right coronary artery with congenital absence of left coronary system. BMJ Case Rep2018;11(1):e228296.
8.
ChoiJHKornblumRN. Pete Maravich’s incredible heart. J Forensic Sci. 1990;35(4):981–986.
9.
MeryCMLawrenceSMKrishnamurthyR. Anomalous aortic origin of a coronary artery: toward a standardized approach. Semin Thorac Cardiovasc Surg. 2014;26(2):110–122.
