Early recruitment of a discontinuous branch pulmonary artery will give the best long-term outcome for congenitally disconnected pulmonary arteries. This may be achieved using a staged approach. Even in low birth weight neonates, a hybrid approach with the first stage consisting of transcervical (via the common carotid artery) patent ductus arteriosus stenting can be performed to recruit the pulmonary artery where conventional treatment strategies may not be feasible or may be associated with higher risk.
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References
1.
KuceraVFiserBTumaSHucinB. Unilateral absence of pulmonary artery: a report on 19 selected clinical cases. Thorac Cardiovasc Surg. 1982;30(3):152–158.
2.
BourosDParePPanagouPTsintirisKSiafakasN. The varied manifestation of pulmonary artery agenesis in adulthood. Chest. 1995;108(3):670–676.
3.
KruzliakPRaoPSNovakMPechanovaOKovacovaG. Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment. Arch Cardiovasc Dis. 2013;106(8-9):448–454.
4.
MurphyDNWinlawDSCooperSGNunnGR. Successful early surgical recruitment of the congenitally disconnected pulmonary artery. Ann Thorac Surg. 2004;77(1):29–35.
5.
MeryCMMolinaKMKrishnamurthyRFraserCDJustinoH. Pulmonary artery resuscitation for isolated ductal origin of a pulmonary artery. J Thorac Cardiovasc Surg. 2014;148(5):2235–2244.
6.
BatliwalaSPMcElhinneyDBPigulaFAMarshallAC. Isolated pulmonary artery arising from a duct: a single center review of diagnostic and therapeutic strategies. J Thorac Cardiovasc Surg. 2014;148(5):2245–2252.
7.
KrammohEKBigrasJLPrsaMLapierreCMiróJDahdahNS. Therapeutic strategies in children with an isolated unilaterally absent proximal pulmonary artery. Pediatr Cardiol. 2010;31(5):607–610.
8.
AzzolinaGEufrateSAlellaA. New approach to catheterization of the heart in infants and children. Br Heart J. 1973;35(6):643–646.