Absent pulmonary valve is a rare congenital heart defect where the pulmonary valve is either absent or rudimentary. It is usually associated with tetralogy of Fallot although it has been reported with other lesions. We present a rare case of absent pulmonary valve associated with transposition of great arteries and non-routable ventricular septal defect that was surgically managed by aortic root translocation.
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References
1.
CheversN. Recherches sur les maladies de l’arteire pulmonaire. Arch Gen Med. 1847;15:488–508.
2.
MillerRALevMPaulMH. Congenital absence of the pulmonary valve. The clinical syndrome of tetralogy of Fallot with pulmonary regurgitation. Circulation. 1962;26(2):266–278.
3.
OvseyevitzJAttieFBuendiaA. Congenital absence of the pulmonary valve leaflets associated with complete transposition of the great arteries. Int J Cardiol. 1982;1(3-4):263–271.
4.
OppidoGCarottiAAlbaneseSBAmodeoAPasquiniLDi DonatoRM. Transposition with absent pulmonary valve syndrome: early repair of a rare case. Ann Thorac Surg. 2001;71(5):1686–1688.
