Sinus venosus defect (SVD) is a deficiency in the sinus venosus portion of the atrium, often associated with partial anomalous pulmonary venous connections. In patients with vein of Galen malformation (VGAM), SVD provides a unique challenge with respect to embolization treatment. In our case, the child had percutaneous device closure of the SVD prior to VGAM embolization. Nine years later, he required surgical removal of the SVD device and Warden procedure due to progressive right-sided cardiac enlargement.
HealeyJEJr. An anatomic survey of anomalous pulmonary veins: their clinical significance. J Thorac Surg. 1952;23(5):433–444.
2.
LasjauniasPLChngSMSachetMAlvarezHRodeschGGarcia-MonacoR. The management of vein of Galen aneurysmal malformations. Neurosurgery. 2006;59(5 suppl 3):S184–S194; discussion S3-13.
3.
McElhinneyDBHalbachVVSilvermanNHDowdCFHanleyFL. Congenital cardiac anomalies with vein of Galen malformations in infants. Arch Dis Child. 1998;78(6):548–551.
4.
FriedmanDMRutkowskiMMadridMBerensteinA. Sinus venosus atrial septal defect associated with vein of Galen malformations: report of two cases. Pediatr Cardiol. 1994;15(1):50–52.
5.
HansenDKanPTReddyGDMohanACJeaALamS. Pediatric knowledge update: approach to the management of vein of Galen aneurysmal malformations in neonates. Surg Neurol Int. 2016;7(suppl 12):S317–S321.
6.
HewittAMorricalBCettaF. Cerebral arteriovenous malformation detected by newborn congenital heart disease screen with echocardiography. Cardiovasc Imaging Case Rep. 2017;1(6):242–244.
7.
DelaneyJWThorellWEHammelJM. Hybrid peratrial double device closure of a patent foramen ovale and sinus venosus defect in an infant with vein of Galen malformation. Catheter Cardiovasc Interv. 2011;78(7):1045–1050.
8.
AhmadNSWalkerIABrewS. Repair of sinus venosus defect in a patient with untreated vein of Galen aneurysmal malformation. Paediatr Anaesth. 2008;18(6):548–553.
