Interrupted aortic arch (IAA) is a rare condition that generally requires surgical correction in the newborn. We report a case of delayed presentation of type A interrupted aortic arch with ventricular septal defect in a 13-year-old female. Single-stage correction without circulatory arrest was accomplished via midline sternotomy approach. Tissue-to-tissue anastomosis was performed without the use of prosthetic material in order to optimize chances for future growth. This simplified technique avoids additional procedures, reduces ischemic time, and prevents problems related to circulatory arrest.
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