We report a two-year-old patient with isomerism of the right atrial appendages, a functionally univentricular heart, and associated totally anomalous pulmonary venous connection. The unusual finding was an intrapulmonary course of the vertical vein. We discuss the anatomical findings, management, and outcome.
NakataTFujimotoYHiroseKOsakiMTosakaYIdeYFunctional single ventricle with extracardiac total anomalous pulmonary venous connection. Eur J Cardiothorac Surg. 2009;36(1):49–56.
MalankarDTalwarSMakhijaNSharmaSChoudharySK. Surgical management of univentricular heart with total anomalous pulmonary venous drainage and intrapulmonary vertical vein. J Card Surg. 2010;25(1):84–86.
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TalwarSChoudharySKMukkannavarSBAiranB. Diaphragmatic fenestration for resistant pleural effusions after the Fontan operation. J Thorac Cardiovasc Surg. 2012;143(1):244–245.
