Perinatal management of severe mitral regurgitation (MR) and aortic stenosis (AS) is difficult; mortality is high, and there are few reports of successful postnatal biventricular repairs. We report a patient with severe MR and AS, diagnosed prenatally, that underwent a fetal aortic valvuloplasty and a successful modified Ross-Konno procedure with concomitant mitral valve repair shortly after birth.
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