Pentalogy of Cantrell is a rare diagnosis consisting of several midline defects of the sternum, abdominal wall, diaphragm, pericardium, and heart. One of the known features is ventricular diverticulum that can represent a technical challenge surgically. This is a follow-up case report of the successful simultaneous resection of a biventricular diverticulum and omphalocele repair after previous report of repair of complex intracardiac disease in the same patient.
CantrellJRHallerJARavitchMM.. A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. Surg Gynecol Obstet. 1958;107(5):602–614.
2.
KorverAMHHaasFFreundMWStrengersJLM.. Pentalogy of Cantrell: successful early correction. Pediatric Cardiol. 2008;29(1):146–149.
3.
AshrafMHGingellRPieroniDDharNSubramanianS.. Congenital diverticulum of the heart of biventricular origin. Thorac Cardiovasc Surg. 1984;32(6):389–391.
4.
BalderrabanoNVizcainoASandovalE. Pentalogy of Cantrell: Forty-two years of experience in the hospital Infantil de Mexico Federico Gomez. World J Pediatric Cong Heart Surg. 2011;2(2):211–218.
5.
OotakiYStrainicJUngerleiderRM.. Pentalogy of Cantrell with double-outlet right ventricle: a case of surgical correction. Cardiol Young. 2011;21(2):235–237.
6.
CarmiRBoughmanJA.. Pentalogy of Cantrell and associated midline anomalies: a possible ventral midline developmental field. Am J Med Genet. 1992;42(1):90–95.
7.
Vasquez-JimenezJFMuehlerEGDaebritzS. Cantrell’s syndrome: a challenge to the surgeon. Ann Thorac Surg. 1998;65(4):1178–1185.
8.
SymbasPNWareRE.. A syndrome of defects of the thoracoabdominal wall, diaphragm, pericardium, and heart: one-stage surgical repair and analysis of the syndrome. J Thorac Cardiovasc Surg. 1973;65(6):914–919.
9.
VanamoKSairanenHLouhimoI.. The spectrum of Cantrell’s syndrome. Pediatr Surg Int. 1991;6:429–433.
10.
MarotoCMarotoEGarcíaEJVallésPDelcánJLArcasR.. Congenital cardiac diverticulum originating from both ventricles. Rev Esp Cardiol. 1991;44(5):351–354.
11.
MarijonEOuPFermontL. Diagnosis and outcome in congenital ventricular diverticulum and aneurysm. J Thorac Cardiovasc Surg. 2006;131(2):433–437.
12.
HalbertsmaFJvan OortAvan der StaakF.. Cardiac diverticulum and omphalocele: Cantrell’s pentalogy or syndrome. Cardiol Young. 2002;12(1):71–74.
