Bilateral segmental agenesis of the internal carotid artery is a rare developmental anomaly. We report a case of congenital bilateral internal carotid arteries segmental agenesis associated with persistent trigeminal artery, vascular ectasia and abnormal configuration brain stem and cerebellum. We postulate that these findings could result from interference in development during the early stages.
AfifiAKGoderskyJCMenezesA: Cerebral hemiatrophy, hypoplasia of internal carotid artery, and intracranial aneurysm. A rare association occurring in an infant. Arch Neurol44: 232–235, 1987.
2.
ChenCJChenSTHsiehFY: Hypoplasia of the internal carotid artery with intercavernous anastomosis. Neuroradiology40: 252–254, 1998.
3.
BeresiniDCHieshimaGBMehringerCM: Bilateral absence of the internal carotid artery with sellar enlargement due to anomalous vascularity. Surg Neurol16: 9–16, 1981.
4.
HattoriTKobayashiHInoueS: Persistent primitive trigeminal artery associated with absence of internal carotid artery. Surg Neurol50: 352–355, 1998.
5.
GozzoliLCrastoSLeombruniS: Magnetic Resonance Angiography in a Case of Agenesis of the Left Carotid Artery Associated with Transellar Intercarotid Anastomosis Agenesia della carotide interna sinistra e anastomosi intercarotidea transellare. Rivista di Neuroradiologia11: 883, 1998.
6.
BodheyNKGuptaAKVarmaDR: CT Angiographic Demonstration of Agenesis of the Internal Carotid Artery with Transsellar Cavernous Collateral and PCA Aneurysm. Rivista di Neuroradiologia17: 664, 2004.
7.
GivenCA2ndHuang-HellingerFBakerMD: Congenital absence of the internal carotid artery: Case reports and review of the collateral circulation. Am J Neuroradiol22: 1953–1959, 2001.
8.
LasjauniasPSantoyo-VazquezA: Segmental agenesis of the internal carotid artery: Angiographic aspects with embryological discussion. Anat Clin6: 133–141, 1984.
9.
PadgetDH: The development of the cranial arteries in the human embryo. Contrib Embryol32: 207–262, 1948.
10.
CaliRLBergRRamaK: Bilateral internal carotid artery agenesis: A case study and review of the literature. Surgery113: 227–233, 1993.
11.
PatelSBarkovichAJ: Analysis and classification of cerebellar malformations. Am J Neuroradiol23: 1074–1087, 2002.
