We report a case of cerebral arteriovenous fistula (AVF) associated with hereditary haemorrhagic telangiectasia (HHT). Although the patient had no symptoms from the cerebral AVF, the AVF was successfully embolised using a two-staged double provocative test. We reviewed the literature of HHT and have concluded that there are two types of cerebral arteriovenous communication in patients with HHT and endovascular embolisation is the most reasonable therapy for the fistula type from the standpoint of its angioarchitecture.
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