Cerebral proliferative angiopathy (CPA) is a rare vascular abnormality and separate from “classical” brain arteriovenous malformations. Haemorrhage due to proliferative angiopathy is rarely reported. We describe the clinical features, imaging findings and targeted endovascular management for a 12-year-old boy having proliferative angiopathy of the posterior fossa presenting with haemorrhage. Targeted endovascular embolisation in CPA is not previously described in the literature. The optimal treatment options for haemorrhagic CPA are debatable, and we wish to highlight the role of targeted treatment for culprit focal lesion demonstrable on imaging.
ChinLSRaffelCGonzalez-GomezIet al.Diffuse arteriovenous malformations: a clinical, radiological, and pathological description. Neurosurgery1992; 31: 863–869.
2.
YasargilMG. Microneurosurgery, Vol IIIA, Stuttgart: Georg Thieme Verlag, 1987.
3.
LasjauniasPLLandrieuPRodeschGet al.Cerebral proliferative angiopathy: Clinical and angiographic description of an entity different from cerebral AVMs. Stroke2008; 39: 878–885.
4.
EllisMJArmstrongDDirksPB. Large vascular malformation in a child presenting with vascular steal phenomenon managed with pial synangiosis. Case report. J Neurosurg Pediatr2011; 7: 15–21.
5.
KonoKTeradaT. Encephaloduroarteriosynangiosis for cerebral proliferative angiopathy with cerebral ischemia. J Neurosurg2014; 121: 1411–1415.
