A thirty-two-year-old woman was operated on for abdominal aortic aneurysm due to vasculo-Behqet's disease. Her aortography showed an aneurysm of curious eggplant-like configuration. At operation, the aneurysm was found to be adhered to the surrounding organ with the severely thickened wall. The diseased aorta was replaced with Y-shaped Dacron graft. Three anastomosis sites were apart from the inflammation and were rolled up with the Teflon felt for reinforcement. Pathology of the diseased wall showed an infiltration of the inflammatory cells with the small-vessel vasculitis due to Behqet's disease. She has had an uneventful postoperative course with a tapering corticosteroid therapy.
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References
1.
1. Behcet HH: Uber rezidivierende, aphthose, durch ein virus verursachte geschwure am mund, am auge und un der genitalien. Derm Wschr 105:1152-1157, 1937.
2.
2. Bartlett ST, McCarthy WJ II, Palmer AS, et al: Multiple aneurysms in Behcet's disease. Arch Surg123:1004-1008, 1988.
3.
3. Ohbuchi T, Yagyu K, Shindo G, et al: A case of vasculo-Behcet's syndrome with thoracic aortic pseudoaneurysm. Jpn J Cardiovasc Surg22:501-504, 1993.
4.
4. Chajek T, Fainaru M: Behcet's disease. Report of 41 cases and a review of the literature. Medicine54:179-196, 1975.
5.
5. Little AG, Zarins CK: Abdominal aortic aneurysm and Behqet's disease. Surgery91:359-362, 1982.
6.
6. Hills EA: Behcet's syndrome with aortic aneurysms. Br Med J4:152-154, 1967.
7.
7. Fauci AS, Haynes BF, Katz P: The spectrum of vasculitis. Ann Intern Med89:660-676, 1978.
8.
8. Nakayama Y, Kosako Y, Okazaki Y, et al: A case of giant popliteal aneurysm with compression neuropathy in Behcet's disease. Jpn J Cardiovasc Surg21:195-199, 1992.
9.
9. Freyrie A, Paragona O, Cenacchi G, et al: True and false aneurysms in Behcet's disease: Case report with ultrastructural observations. J Vasc Surg17:762-767, 1993.
10.
10. Smith EJ, Abulafi M, McPherson GA, et al: False aneurysm of the abdominal aorta in Behcet's disease. Eur J Vasc Surg5:481-484, 1991.
