DeBakey-Type IlIb Aortic Dissection with Multiple Aneurysmal Changes of the Peripheral Arteries

Abstract

A forty-four-year-old woman presented with a DeBakey-type IlIb dissecting aneurysm, multiple aneurysmal dilatation of the coronary arteries, and a “string-of-beads” appearance of the peripheral arteries (due to cystic medial necrosis and intimal hyperplasia). Upon assessment of her family history and multiple vascular involvement secondary to cystic medial necrosis, an incomplete Marfan's syndrome was suggested. This rare case of multiple aneurysmal changes to the great and peripheral arteries is presented with special reference to the radiographic and morphologic manifestations.