Polysplenia/heterotaxy syndrome is a rare condition involving multiple gastrointestinal, vascular, and cardiac malformations. We present a previously unreported association of aortic coarctation, double superior vena cava, a left-hand side inferior vena cava with hemiazygos vein continuation and a right retroaortic renal vein with polysplenia/heterotaxy syndrome. Multidetector computed tomography with multiplanar reconstruction images were useful in the detection of these abnormalities.
Peoples WM, Moller JH, Edward JEPolisplenia: a review of 146 cases. Pediatr Cardiol . 1983;4(2):129-137.
2.
Plata-Muñoz JJ, Hernández-Ramírez D., Anthón FJ, Podgaetz E., Avila-Flores F., Chan C.Polysplenia syndrome in the adult patient. Case report with review of the literature. Ann Hepatol. 2004;3(3):114-117.
3.
Seo HI, Jeon TY, Sim MS, Kim S.Polysplenia syndrome with preduodenal portal vein detected in adults . World J Gastroenterol. 2008;14(41):6418-6420.
4.
Ahmetoğlu A., Koşucu P., Sarı A., Gümele HRPolispleni sendromunda radyolojik bulgular . Tanısal ve Girişimsel Radyoloji Dergisi. 2002;8(4):510-512.
5.
Kondrachuk O. , Yalynska T., Yemets I.Heterotaxy syndrome (mirror-image dextrocardia, coarctation of the aorta, polysplenia): a previously unreported association . Pediatr Cardiol.2009;30(6): 864-865.
Winer-Muram HT , Tonkin Ild.The spectrum of heterotaxic syndromes . Radiol Clin North Am. 1989;27(6):1147-1170.
8.
Van de Perre S., Vanhoenacker FM, Petré C., Van Doorn J., De Schepper AMHeterotaxy syndrome. JBR-BTR . 2004;87(3):158-159.
9.
Applegate KE , Goske MJ, Pierce G., Murphy D.Situs revisited: imaging of the heterotaxy syndrome. Radiographcs. 1999;19(4): 837-852.
10.
Ooshima I., Maruyama T., Ootsuki K., Ozaki M.Predodenal portal ven in the adult. J Hepatobiliary Pancreat Surg. 1998;5(4):455-458.
11.
Soler R., Rodríguez E., Comesaña ML, Pombo F., Marini M.Agenesis of the dorsal pancreas with polysplenia syndrome: CT features . J Comput Assist Tomogr. 1992;16(6):921-923.
