In contrast to the application of applied behavior analysis principles in autism and developmental disorders, there is a general paucity of research examining effectiveness of cognitive-behavioral interventions with individuals with mental retardation and even less with mental retardation of a specific etiology. The authors present a case study of cognitive-behavioral treatment for emotional and behavioral difficulties in a young man with Williams syndrome, a genetic disorder characterized by developmental and psychosocial impairments. Following a functional assessment, an intensive intervention was designed and implemented to address social skills difficulties, obsessions, and compulsions. Results suggest that cognitive-behavioral interventions may be promising with this population. Obstacles encountered and lessons learned are discussed.
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