CreutzfeldtHG. Uber eine eigenartige herdformige Erkrankung des Zentralnervensystems. Z ges Neurol Psychiat1920; 57:1–18.
2.
JakobA. Uber eigenartige Erkrankungen des Zentralnervensystems mit bemerkenswerten anatomischen Befunde (Spastische Pseudosklerose-Encephalomyelopathie mit disseminierten Degenerations-herden). Z ges Neurol Psychiat1921; 64:147–228.
3.
Richardson JnEPMastersCL. The nosology of Creutzfeldt-Jakob Disease and conditions related to the accumulation of PrPCJD in the nervous system. Brain Pathol1995; 5:33–41.
4.
MastersCLRichardsonEP. Subacute spongiform encephalopathy (Creutzfeldt-Jakob disease). The nature and progression of spongiform change. Brain1978; 101:559–88.
5.
GibbsCJGajdusekDCAsherDM. Creutzfeldt-Jakob disease (subacute spongiform encephalopathy): Transmission to the chimpanzee. Science1968; 161:388–9.
6.
GajdusekDCZigasV. Degenerative disease of the central nervous system in New Guinea: the endemic occurrence of ‘kuru’ in the native population. New Engl J Med1957; 257:974–8.
7.
GerstmannJStrausslerEScheinkerI. Uber eine eigenggartige hereditarfamiliare Erkrankung des Zentralnervensystems, zugleich ein Beitrag zur Frage des vorzeitigen lokalen Alterns. Z ges Neurol Psychiat1936; 154:736–2.
8.
KimberlinRH. Scrapie. Brit Vet J1981; 137:105–12.
9.
CuilleJChelleP-L. La malade dite temblente du mouton est-elle inoculable?Comptes Rendu Acad Sci1936; 203:1552–4.
10.
GajdusekDCGibbsCJAlpersMP. Experimental transmission of a kuru-like syndrome in chimpanzees. Nature1966; 209:794–6.
11.
BastianFO (ed).Creutzfeldt-Jakob disease and other transmissible human spongiform encephalopathies. St Louis: Mosby Year Book 1991.
12.
BrownPPreeceMAWillRG. ‘Friendly fire’ in medicine: hormones, homografts and Creutzfeldt- Jakob disease. Lancet1992; 340:24–7.
13.
DuffyPWolfJCollinsG. Possible person-to-person transmission of Creutzfeldt-Jakob disease. New Engl J Med1974; 290:692.
14.
AdamsDHCasparyEAFieldEJ. Susceptibility of scrapie agent to ionising radiation. Nature1969; 221:90–1.
15.
PattisonI. Resistance of the scrapie agent to formalin. J Comp Pathol1965; 75:159–64.
16.
GriffithsJ. Self replication and scrapie. Nature1967; 215:1043–4.
17.
PrusinerSB. Novel proteinaceous infectious particles cause scrapie. Science1982; 216:136–44.
18.
PrusinerSB. Biology and genetics of prion disease. Ann Rev Microbiol1994; 48:655–86.
19.
GoldfarbLGBrownPCervenakovaLGajdusekDC. Molecular genetic studies of Creutzfeldt-Jakob disease. Mol Neurobiol1994; 8:89–97.
20.
MastersCLGajdusekDCGibbsCJ. Creutzfeldt-Jakob disease virus isolations from the Gerstmann Straussler syndrome with an analysis of the various forms of amyloid plaque deposition in the virus induced spongiform encephalopathies. Brain1981; 104:559–88.
21.
PalmerMSDrydenAJHughesJTCollingeJ. Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease. Nature1991; 352:340–2.
22.
CollingeJPalmerMSDrydenAJ. Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease. Lancet1991; 337:1441–2.
23.
ParchiPCastellaniRCapellariS. Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol1996; 39:669–80.
24.
MacDonaldSTSutherlandKIronsideJW. Prion protein genotype and pathological phenotype studies in sporadic Creutzfeldt-Jakob disease. Neuropathol Appl Neurobiol1996; 22:285–92.
25.
BrownPCathalaFRaubertasRF. The epidemiology of Creutzfeldt-Jakob disease: conclusion of a 15-year investigation in France and review of the world literature. Neurology1987; 37:295–304.
26.
WillRG. Epidemiology of Creutzfeldt-Jakob disease. Brit Med Bull1993; 49:960–70.
27.
WillRG. Surveillance of prion diseases in humans. In: BakerHFRidleyRM. Prion diseases. New Jersey: Humana Press1996, 119–37.
28.
CousensSNZeidlerMEsmondeTF. Sporadic Creutzfeldt-Jakob disease in the United Kingdom: analysis of epidemiological surveillance data for 1970–96. Brit Med J1997; 315:389–96.
29.
BortoneEBettoniLGiorgiC. Reliability of EEG in the diagnosis of Creutzfeldt-Jakob disease. Electroenceph Clin Neurophysiol1994; 90:323–30.
30.
WellsGAHScottACJohnsonCY. A novel progressive spongiform encephalopathy in cattle. Vet Rec1987; 121:419–20.
31.
WilesmithJWRyanJBMAtkinsonMJ. Bovine spongiform encephalopathy. Epidemiological studies on the origin. Vet Rec1991; 128:199–203.
32.
AndersonRMDonnellyCAFergusonNM. Transmission dynamics and epidemiology of BSE in British cattle. Nature1996; 382:779–88.
33.
KirkwoodJKCunninghamAA. Epidemiological observations on spongiform encephalopathies in captive wild animals in the British Isles. Vet Rec1994; 135:296–303.
34.
WyattJMPearsonGRSmerdonTN. Naturally occurring scrapie-like spongiform encephalopathy in five domestic cats. Vet Rec1991; 129:233–6.
35.
WilloughbyKKellyDFLyonDGWellsGAH. Spongiform encephalopathy in captive puma (Felis concolor). Vet Rec1992; 131:431–4.
36.
Delasnerie-LaupretreNPoserSPocchiariM. Creutzfeldt-Jakob disease in Europe. Lancet1995; 346:898.
37.
WillRGIronsideJWZeidlerM. A new variant of Creutzfeldt-Jakob disease in the UK. Lancet1996; 347:921–5.
38.
ZeidlerMBamberRWKDickensCM. New variant Creutzfeldt-Jakob disease: psychiatric features. Lancet1997; 350:908–11.
39.
ZeidlerMStewartGEBarracloughCR. New variant Creutzfeldt-Jakob disease: neurological features and diagnostic tests. Lancet1997; 350:903–7.
40.
ChazotGBroussolleELaprasCLKoppN. New variant of Creutzfeldt-Jakob disease in a 26-year old French man. Lancet1996; 347:1181–2.
41.
IronsideJWSutherlandKBellJE. A new variant of Creutzfeldt-Jakob disease: neuropathological and clinical features. Cold Spring Harbor Symp Quant Biol1996; 61:523–30.
42.
FraserH. The pathogenesis and pathology of scrapie. In: TyrellDAJAspects of slow and persistent virus infections. The Hague: Martinus Nijhoff1979, 30–58.
43.
BellJEIronsideJW. Neuropathology of spongiform encephalopathy in humans. Brit Med Bull1993; 49:738–77.
44.
de SilvaRIronsideJWMcCardleLEsmondeTGF. Neuropathological phenotype and prion protein genotype: correlation in sporadic Creutzfeldt-Jakob disease. Neurosci Lett1994; 179:50–2.
45.
HillAFZeidlerMIronsideJWCollingeJ. Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy. Lancet1997; 349:99–100.
46.
LudlamC. New variant Creutzfeldt-Jakob disease and treatment of haemophilia. Lancet1997; 350:1704.
47.
EsmondeTFGWillRGSlatteryJM. Creutzfeldt-Jakob disease and blood transfusion. Lancet1993; 341:205–6.
48.
LasmezasCIDeslysJ-PPDemalmayR. BSE transmission to macaques. Nature1996; 381:743–4.
49.
CollingeJSidleKCLMeadsJ. Molecular analysis of prion strain variation and the aetiology of ‘'new variant'’ CJD. Nature1996; 383:685–90.
50.
HillAFDesbruslaisMCJoinerS. The same prion strain causes nvCJD and BSE. Nature1997; 389:448–50.
51.
BruceMEChreeAMcConnellI. Transmission of bovine spongiform encephalopathy and scrapie to mice. Strain variation and the species barrier. Phil Trans R Soc Lond1994; 343:405–11.
52.
BruceMEWillRGIronsideJW. Transmissions to mice indicate that ‘'new variant'’ CJD is caused by the BSE agent. Nature1997; 389:498–501.
53.
PattisonJAlmondJ. Human BSE. Nature1997; 389:437–8.
54.
CousensSNVynnynckyEZeidlerM. Predicting the CJD epidemic in humans. Nature1997; 385:197–8.